Autosomal dominant polycystic kidney disease presenting with hepatic encephalopathy.

نویسندگان

  • Mohammad Alkali
  • A U Hamidu
  • Auwal Modu
چکیده

Dear Sir, Autosomal dominant polycystic kidney disease (ADPKD) is a multi-systemic and progressive disorder characterized by formation of cysts in ductal organs particularly the kidneys, liver, pancreas, gastro-intestinal tract, the central nervous system and the cardiovascular system.[1,2] The disease may occur anytime in life, including in utero in contrast with its previous name “adult polycystic kidney” which suggests affectation of only adults.[3] ADPKD is the most frequent genetic cause of renal failure in adults and is slightly more severe in males than in females while symptoms generally increase with age.[1]

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عنوان ژورنال:
  • Annals of African medicine

دوره 8 2  شماره 

صفحات  -

تاریخ انتشار 2009