Autosomal dominant polycystic kidney disease presenting with hepatic encephalopathy.
نویسندگان
چکیده
Dear Sir, Autosomal dominant polycystic kidney disease (ADPKD) is a multi-systemic and progressive disorder characterized by formation of cysts in ductal organs particularly the kidneys, liver, pancreas, gastro-intestinal tract, the central nervous system and the cardiovascular system.[1,2] The disease may occur anytime in life, including in utero in contrast with its previous name “adult polycystic kidney” which suggests affectation of only adults.[3] ADPKD is the most frequent genetic cause of renal failure in adults and is slightly more severe in males than in females while symptoms generally increase with age.[1]
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عنوان ژورنال:
- Annals of African medicine
دوره 8 2 شماره
صفحات -
تاریخ انتشار 2009